General

What is PFAPA syndrome?

What is PFAPA syndrome?

The most common causes of recurrent fever in children with ear inflammation, throat and urinary tract infections, voicing that. Yilmazer 'A child may experience upper respiratory tract infection 7-8 times a year. The number of these infections can reach 10-12 in nursery and kindergarten. However, it should not be forgotten that recurrent fever syndromes occur rhythmically and in cases where fever persists for a long time despite treatment.

What is PFAPA Syndrome?

In all of the recurrent fever syndromes, the body reacts as if it had encountered a germ, without a microbial condition causing the fever. For this reason, they are often diagnosed with throat or bowel infections and use intensive antibiotics and antipyretics. However, despite intensive treatment, the symptoms persist for 3-10 days and eventually resolve.

Each time the same picture is repeated and patients have tonsil or appendicitis surgery from time to time. One of the most common recurrent fever is PFAPA syndrome.

Fever attacks lasting 3-7 days are accompanied by aphthae in the mouth, throat inflammation and swelling of the gland in the neck. In some cases, headache and abdominal pain may accompany. When the fever is between 38-41ºC, it is more or less predictable by families.

Pay attention to these symptoms!

• If your child's fever lasts 3-7 days (average 5 days) and falls suddenly,

• In addition to fever, abdominal pain, nausea, vomiting, sweating, tremor, muscle-bone and joint pain,

• If the glands on the neck become swollen on both sides,

• If there is growth in the liver and spleen,

• If aphthas occurred in the mouth (these aphthas are usually painless and heal quickly.)

• If the fever tends to fall suddenly and the general state of fever recovers quickly and is completely normal between attacks; your child may have PFAPA syndrome. Although PFAPA syndrome is a frequent episode, the development and growth of the child is not affected. In blood tests, there is an increase in findings suggestive of severe inflammation in the patient. However, microbes cannot be detected in both throat cultures and other materials.

The most important feature of PFAPA syndrome; As the age grows, the breaks are opened and spontaneous healing occurs within 4-8 years. The diagnosis of the disease is made by the presence of the above findings after the elimination of other causes of recurrent fever, especially Familial Mediterranean Fever.

Patients diagnosed as PFAPA syndrome are given cortisone treatment at the beginning of febrile episodes and the disease is quickly controlled. With this treatment, the interval between attacks is often opened.

In cases of pfapa syndrome that cannot be controlled with cortisone treatment, nasal flesh and tonsil surgeries are also recommended. In cases where fever recurs rhythmically, recurrent fever syndromes should be considered and necessary treatment should be planned.